A case of an ameloblastic carcinoma in an unusual situation in the maxilla is presented. The lesion is characterized histologically by areas with features of a typical ameloblastoma and areas with anaplastic transformation. A Caldwell-Luc operation was followed by a recurrence after 3 years. Due to the advanced age and poor general health of the patient an enlarged, but not radical operation was performed. There is no evidence of metastatic tumour.