NMDA receptor encephalitis--expanding the clinical spectrum

BMJ Case Rep. 2011 Jul 28:2011:bcr1220103579. doi: 10.1136/bcr.12.2010.3579.

Abstract

A young woman presented with memory problems of subacute onset. Imaging was normal. She was admitted with severe complex partial status epilepticus requiring intensive care support and ventilation. Fits proved difficult to control requiring high dose anticonvulsants. She developed a profound amnesic syndrome. A clinical diagnosis of autoimmune encephalitis was considered and she was treated with intravenous steroids with an excellent cognitive outcome. She continues to have occasional seizures.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Diagnosis, Differential
  • Diagnostic Imaging
  • Electrocardiography
  • Electroencephalography
  • Encephalitis / diagnosis
  • Encephalitis / metabolism*
  • Encephalitis / therapy*
  • Female
  • Humans
  • Immunotherapy
  • Plasma Exchange
  • Receptors, N-Methyl-D-Aspartate / metabolism*
  • Status Epilepticus / diagnosis
  • Status Epilepticus / metabolism*
  • Status Epilepticus / therapy
  • Steroids / therapeutic use

Substances

  • Receptors, N-Methyl-D-Aspartate
  • Steroids