Pulmonary lymphangioleiomyomatosis associated with retroperitoneal lymphangioleiomyomas

BMJ Case Rep. 2012 Jan 18:2012:bcr0920114808. doi: 10.1136/bcr.09.2011.4808.

Abstract

A 36-year-old woman presented with worsening symptoms of abdominal pain, diarrhoea, low fever, dyspnoea on exertion and bilateral leg during the last 2 months. Chest radiograph showed mild diffuse reticular pattern with preserved lung volumes. Lung high resolution CT disclosed multiple thin-walled lung cysts throughout the lungs bilaterally with no zonal predominance and with normal intervening parenchyma and abdominal CT revealed bilateral retrocrural and retroperitoneal hypodense masses. Imaging findings were consistent with lymphangioleiomyomatosis.

Publication types

  • Case Reports

MeSH terms

  • Abdominal Neoplasms / complications*
  • Abdominal Neoplasms / diagnosis
  • Abdominal Neoplasms / diagnostic imaging
  • Adult
  • Diagnosis, Differential
  • Female
  • Humans
  • Lung Neoplasms / complications*
  • Lung Neoplasms / diagnosis
  • Lung Neoplasms / diagnostic imaging
  • Lymphangioleiomyomatosis / complications*
  • Lymphangioleiomyomatosis / diagnosis
  • Lymphangioleiomyomatosis / diagnostic imaging
  • Lymphangiomyoma / complications*
  • Lymphangiomyoma / diagnosis
  • Lymphangiomyoma / diagnostic imaging
  • Retroperitoneal Space* / diagnostic imaging
  • Tomography, X-Ray Computed