You are here

  • Home
  • Archive
  • Volume 2018, Issue
  • Severe pulmonary hypertension associated with hepatic arteriovenous malformation in a patient with hereditary haemorrhagic telangiectasia

Article Text

Article menu
Download PDFPDF
Rare disease
CASE REPORT
Severe pulmonary hypertension associated with hepatic arteriovenous malformation in a patient with hereditary haemorrhagic telangiectasia
  1. Sakolwat Montrivade1,
  2. Patinya Maneesow2,
  3. Thamonwan Osotthanakorn2,
  4. Pairoj Chattranukulchai1
  1. 1Division of Cardiovascular Medicine, Department of Medicine, Faculty of Medicine, Chulalongkorn University, King Chulalongkorn Memorial Hospital, Bangkok, Thailand
  2. 2Faculty of Medicine, Chulalongkorn University, King Chulalongkorn Memorial Hospital, Bangkok, Thailand
  1. Correspondence to Dr Sakolwat Montrivade, sakolmontri{at}hotmail.com

Summary

We report a case of 46-year-old Asian woman with a history of recurrent epistaxis who presented with dyspnoea on exertion. Physical examination revealed mucocutaneous telangiectasias and signs of heart failure. Further evaluation showed huge hepatic arteriovenous malformation and severe pulmonary hypertension. This case demonstrates an uncommon manifestation of hereditary haemorrhagic telangiectasia presented with severe pulmonary hypertension.

  • cardiovascular medicine
  • heart failure

https://doi.org/10.1136/bcr-2018-226067

Statistics from Altmetric.com

    Request Permissions

    If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

    View Full Text

    Footnotes

    • Contributors SM: was the primary author and provided clinical history and treatment of the patient. TO and PM: co-authors. PC: reviewed echocardiography and CT imagings as well as edited full paper.

    • Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.

    • Competing interests None declared.

    • Patient consent Obtained.

    • Provenance and peer review Not commissioned; externally peer reviewed.