Article Text
PDF
Summary
Primary renal angiosarcoma is an exceedingly rare and aggressive neoplasm. Although it may occur in youth, this tumour is frequently reported in the sixth and seventh decades of life. The clinical presentation is frequently varied. Pathogenesis remains largely unknown and it has overlapping features with other tumours of the kidney. Current treatment options include variable combinations of surgery, chemotherapy and radiotherapy. Reports regarding the disease prognosis and natural history are limited. In this article, we chronicle the case of a patient with primary renal angiosarcoma presenting at an advanced stage as a widely metastasised tumour. Additionally, we undertake here a brief literature review highlighting the rarity and aggressiveness of this condition, its poor prognosis, and the lack of specific management guidelines.
- oncology
- urological cancer
Statistics from Altmetric.com
Footnotes
Contributors HTL: performed the literature review, drafted the manuscript, formulated the data table and reviewed the manuscript. FI: designed the study, performed the literature review, drafted the manuscript, revised the manuscript critically for important intellectual content and gave the final approval for the version published. AM: contributed to the case presentation. GI: provided the histopathological slides.
Funding The authors have not declared a specific grant for this research from any funding agency in the public, commercial or not-for-profit sectors.
Competing interests None declared.
Patient consent Obtained.
Provenance and peer review Not commissioned; externally peer reviewed.