Bland-White-Garland syndrome on coronary CT angiography
- 1Department of Radiology, Centro Hospitalar de Lisboa Ocidental EPE, Lisboa, Portugal
- 2Department of Paediatric Cardiology, Centro Hospitalar de Lisboa Ocidental EPE, Lisboa, Portugal
- Correspondence to Dr Ana Coutinho Santos, a.icoutinho.santos{at}gmail.com
- Accepted 25 March 2018
- Published 10 April 2018
Description
A 2-month-old infant presented with poor weight gain, feeding intolerance and cardiomegaly on chest radiography. Transthoracic echocardiography showed severe left ventricular dilatation and dysfunction, left atrial dilatation, moderate mitral regurgitation and doubtful origin of left coronary artery (LCA). Cardiac catheterisation did not identify the origin of LCA from the aorta. Coronary CT angiography (128-multidetector CT, retrospective ECG-gated with restrictive dose modulation, 70 kVs, 1.2 mSv) revealed the origin of the LCA from the pulmonary artery trunk/root junction, immediately above the sinus of Valsalva and was consistent with remaining echocardiography findings (figure 1). The right coronary artery had normal origin. After surgical reimplantation of the LCA in the ascending aorta there was good …