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BMJ Case Reports 2018; doi:10.1136/bcr-2017-223232
  • Rare disease
  • CASE REPORT

Follicular dendritic cell sarcoma of the porta hepatis

  1. Brant G Wang3
  1. 1Virginia Commonwealth University School of Medicine, Inova Fairfax Hospital, Falls Church, Virginia, USA
  2. 2Department of Surgery, Inova Fairfax Hospital, Falls Church, Virginia, USA
  3. 3Department of Pathology, Inova Fairfax Hospital, Falls Church, Virginia, USA
  1. Correspondence to Jay A Patel, patelja3{at}vcu.edu
  • Accepted 28 January 2018
  • Published 8 February 2018

Summary

Follicular dendritic cell (FDC) sarcoma is a very rare neoplasm which commonly involves the lymph nodes and less commonly involves extranodal organs such as the liver. Most cases of FDC sarcoma are idiopathic, however some cases are associated with other disease states. Management of FDC sarcoma is primarily focused on surgical resection of the mass, and secondarily focused on radiotherapy, chemotherapy and/or biologic pharmacotherapy. We report the case of a patient who was found to have FDC sarcoma presenting as an obstructing mass of the porta hepatis, a manifestation which does not appear to be reported in the literature.

Footnotes

  • Contributors JAP, JBP and BGW have all contributed to the content in this manuscript.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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