BMJ Case Reports 2018; doi:10.1136/bcr-2017-221505
  • Rare disease

Follicular dendritic cell sarcoma of the duodenum: an extremely rare entity

  1. Niall Swan2
  1. 1National Centre for Hepatopancreatobiliary Surgery and Liver/Pancreas Transplant, St Vincent’s University Hospital, Dublin, Ireland
  2. 2Department of Histopathology, St Vincent’s University Hospital, Dublin, Ireland
  1. Correspondence to Mr Atakelet Ferede, aferede75{at}
  • Accepted 30 January 2018
  • Published 11 February 2018


Extranodal follicular dendritic cell sarcoma (FDCS) is a very rare tumour, only reported in case reports and case series. It poses diagnostic and management challenge both to the clinician and pathologist. We present such a rare case of duodenal FDCS in a 56-year-old woman who was recently managed in our institution. Repeated pre surgical biopsies were non-diagnostic and the final diagnosis was made only after surgical excision of the tumour and with the help of histopathological and immunohistochemical studies. The patient had a complete en block resection of the tumour and was discharged home well 5 days postsurgery. To the best of our knowledge, this is the first case of FDCS reported arising from the duodenum.


  • Contributors AF and RO’C: wrote the manuscript and conducted literature search. ATS and NS: contributed to the manuscript and edited the final draft.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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