BMJ Case Reports 2017; doi:10.1136/bcr-2017-220434
  • Unusual association of diseases/symptoms

Saddle-nose and bilateral cauliflower ear deformities with pyoderma gangrenosum-like ulcers, cavitary pulmonary lesions, digital gangrene and pulselessness in a young female

  1. Kaushal K Verma1
  1. 1Department of Dermatology and Venereology, All India Institute of Medical Sciences, New Delhi, Delhi, India
  2. 2Department of Radiodiagnosis, All India Institute of Medical Sciences, New Delhi, Delhi, India
  1. Correspondence to Professor Kaushal K Verma, prokverma{at}
  • Accepted 19 May 2017
  • Published 15 June 2017


We report a young female who presented with saddle-nose and bilateral cauliflower ear deformities along with pyoderma gangrenosum-like ulcers, digital gangrene and pulselessness. Subsequently, she was found to have bilateral conductive hearing loss, a corneal opacity, mild aortic regurgitation and radiological evidence of cavitary changes in lungs and aortoarteritis. Our patient had a constellation of symptoms which posed a diagnostic challenge. Finally, a diagnosis of relapsing polychondritis with several unusual features was made. Overlap with Takayasu’s arteritis and granulomatosis with polyangitis, which has been reported rarely in the literature, cannot be excluded.


  • Contributors SS: resident in charge of case and preparation of manuscript. VG: resident in charge of case and editing of manuscript. AC: preparation of manuscript and expert radiological opinion. KKV: editing of manuscript.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.

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