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CASE REPORT
Wunderlich's syndrome as a manifestation of polyarteritis nodosa
  1. Pedro Beirão1,
  2. Lídia Teixeira2,
  3. Patrícia Pereira1,
  4. Margarida Lopes Coelho1
  1. 1Department of Internal Medicine, Hospital Garcia de Orta, Almada, Portugal
  2. 2Department of Rheumatology, Hospital Garcia de Orta, Almada, Portugal
  1. Correspondence to Dr Pedro Beirão, pbeirao{at}gmx.com

Summary

Wunderlich syndrome is a rare clinical entity characterised by spontaneous renal haemorrhage that can be life-threatening and requires emergency attention. The most frequent aetiologies are renal tumours and vascular diseases. The authors report a case of a patient admitted with hypovolaemic shock due to a retroperitoneal haematoma in the context of polyarteritis nodosa (PAN). Prognosis of untreated PAN is very poor with 13% 5-year survival rate. Therefore, early recognition of disease and proper treatment with immunosuppressors will prevent catastrophic complications and improves survival.

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Footnotes

  • Contributors PB is responsible for design of the case report, acquisition of data and writing of the main body of the work. LT is responsible for review and acquisitions/writing of the parte concerning rheumatological treatment and follow-up. PP is responsible for review and choice of images. MLC is responsible for global review.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.