Article Text

Download PDFPDF
CASE REPORT
Rumpel-Leede phenomenon in a patient with adult-onset Still's disease
  1. Jacob Trygve Lambdin1,
  2. Catherine Mackenzie2
  1. 1George Washington University School of Medicine and Health Sciences, Arlington, Virginia, USA
  2. 2George Washington University School of Medicine and Health Sciences, Stouffville, Ontario, Canada
  1. Correspondence to Jacob Trygve Lambdin, jlambdin{at}gwu.edu

Summary

Rumpel-Leede phenomenon (RLP), also known as acute capillary rupture syndrome (ACRS), is a rare occurrence where distal dermal capillaries rupture in response to a proximal compressive force, such as a blood pressure cuff or tourniquet. This phenomenon has been reported to occur in states of vascular fragility such as long-term steroid use, hypertension or diabetes mellitus. Here, we provide a report of RLP occurring secondary to tourniquet application in a 26-year-old woman with adult-onset Still's disease (AOSD) and a recent drug rash. In this case, the cause of the phenomenon is most likely multifactorial. Likely contributing factors include long-term steroid use for the treatment of AOSD, and increased vascular permeability secondary to the drug rash. Patients and clinicians should be aware that the treatment of AOSD may induce a state of capillary fragility and they should work together to minimise the risk of complications.

Statistics from Altmetric.com

Request Permissions

If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

Footnotes

  • Contributors JTL is the primary guarantor and primary author who identified and managed the case, and also performed planning and literature review. CM is the coauthor who performed editing and literature review.

  • Competing interests None declared.

  • Patient consent Obtained.

  • Provenance and peer review Not commissioned; externally peer reviewed.