Summary

We report the case of a 9-week-old boy with cystic fibrosis (CF) who presented with intestinal obstruction. He was initially diagnosed with distal intestinal obstruction syndrome (DIOS) and started on laxatives and gastrograffin. This conservative management was unsuccessful and he therefore underwent an exploratory laparotomy. Despite not having undergone any previous surgery, extensive intra-abdominal adhesions were identified as the cause of the intestinal obstruction. The only previous abdominal pathology occurred in the neonatal period prior to his diagnosis of CF, when he was managed conservatively for possible necrotising enterocolitis. We hypothesise that this episode was associated with a subclinical bowel perforation that led to the formation of intra-abdominal adhesions. Although DIOS is the commonest cause of intestinal obstruction in children with CF, this case highlights that surgical causes should always be considered. It also demonstrates that the intra-abdominal adhesions can occur in the absence of previous surgery.