Summary

Pleomorphic adenoma is the most common epithelial tumour of the lacrimal gland in adults. It is rare in children less than 10 years. The low incidence in children can lead to low index of suspicion and increased likelihood of misdiagnosis. Incomplete treatment can lead to malignant transformation or recurrence. High index of suspicion is necessary for prompt diagnosis in children younger than 10 years. We describe a rare case of lacrimal gland pleomorphic adenoma (LGPA) in a 7-year-old child. Only four cases have so far been reported in the literature in children younger than 10 years. We emphasise the importance of CT scan and ultrasound-guided fine needle in the diagnosis of LGPA in children.