BMJ Case Reports 2012; doi:10.1136/bcr-2012-007837
  • Unusual association of diseases/symptoms

Frontal linear scleroderma en coup de sabre associated with epileptic seizure

  1. Perihan Oztürk1
  1. 1Department of Dermatology, Sütçü İmam University, Kahramanmaraş, Turkey
  2. 2Department of Radiology, Sütçü İmam University, Kahramanmaraş, Turkey
  1. Correspondence to Dr Mehmet Fatih Inci, drfatihinci{at}


Linear scleroderma is a rare variant of localised scleroderma, which is usually seen in childhood and during the adolescent period, and can cause severe functional morbidity as well as cosmetic and psychological problems. Although its ethiopathogenesis is yet obscure, autoimmunity, local ischaemia and injuries, vaccination, irradiation, vitamin K injections, Borrelia burgdorferi and Varicella infections have been incriminated. A 4-year-old girl who had been followed up for about 18 months with diagnosis of epilepsy had a colour discolouration and depression that first appeared 1 year ago and then progressed on her left frontal region. Her CT scan showed a thinning in the frontal bone and depression in the frontal region. These findings are described as ‘en coup de sabre’ a rare form of linear scleroderma localised at the frontal region of the scalp. In this paper, we present clinical and radiological findings of a 4-year-old girl with epileptic seizures that started 1 year before the onset of the lesion of linear scleroderma.

Register for free content

The full text of all Editor's Choice articles and summaries of every article are free without registration

The full text of Images in ... articles are free to registered users

Only fellows can access the full text of case reports (apart from Editor's Choice) - become a fellow today, or encourage your institution to, so that together we can grow and develop this resource

Don't forget to sign up for content alerts so you keep up to date with all the case reports as they are published, and let us know what you think by commenting on the Editor's blog

Navigate This Article