Ataxia, hypoplastic vermis and keyhole connection sign: is it the variant form of Dandy-Walker complex?
- Department of Neurology, Sulaimaniya General Teaching Hospital, Sulaimaniya City, Iraq
- Correspondence to Dr Osama S M Amin, dr.osama.amin{at}gmail.com
Description
A 12-year-old girl has a progressive instability of stance and gait since the age of 2 years. She demonstrates mild mental subnormality and signs of cerebellar incoordination. A diagnosis of an ataxic form of cerebral palsy was made at the age of 3 years. When she was 9 years old, she started to develop occasional vomiting and headache which were ascribed to ‘hydrocephalus’. Accordingly, shunting surgery was performed (figure 1). Both headaches and vomiting remarkably improved; however, the cerebellar dysfunction remained. Her up-to-date brain MRI is shown (figure 2).
Axial non-contrast CT brain scan of the patient, which was done 3 years ago. Note the site of the shunt (yellow arrow), which was placed …
