Article Text

Download PDFPDF
Rare disease
Reversible steatohepatosis in a young boy with brittle type 1 diabetes mellitus: mauriac syndrome
  1. Makardhwaj Sarvadaman Shrivastava,
  2. Atul Vijay Palkar,
  3. Namita J Padwal,
  4. Nivedita Moulick
  1. Department of Internal Medicine, Lokmanya Tilak Municipal Medical College and General Hospital, Mumbai, India
  1. Correspondence to Dr Makardhwaj Sarvadaman Shrivastava, makar_in{at}rediffmail.com

Summary

A 14-year-old male, diagnosed case of type 1 diabetes mellitus since 1 year, presented with uncontrolled blood glucose levels, non-compliance with insulin therapy and recurrent admissions with diabetic ketoacidosis. His blood glucose levels were difficult to control with wide fluctuations in insulin requirement. He had absent secondary sexual characteristics and hepatomegaly. Liver biopsy showed macrovesicularsteatosis without fibrosis or inflammation. Many glycogenated nuclei were present. He was started on intensive insulin therapy, whereby he showed subsequent regression of hepatomegaly and onset of pubertal spurt.

Statistics from Altmetric.com

Request Permissions

If you wish to reuse any or all of this article please use the link below which will take you to the Copyright Clearance Center’s RightsLink service. You will be able to get a quick price and instant permission to reuse the content in many different ways.

Footnotes

  • Competing interests None.

  • Patient consent Obtained.