Summary

Rhabdomyosarcoma (RMS) is usually considered a childhood soft tissue tumour. It normally arises within extremities, head and neck region and the genitourinary system. Common sites in the genitourinary tract include the urinary bladder, prostate and paratesticular soft tissues. It can arise at unusual sites but very rarely.1 RMS is more common in males as compared to females and two-thirds of the cases are diagnosed in children aged 6 years or younger with a smaller incidence peak in mid-adolescence.2 The annual incidence is four to seven per million children of 20 years or younger.3 Approximately 350 cases are diagnosed per year in the USA. Unfortunately, statistics of RMS are not known for Pakistan.