Cardiac sarcoidosis mimicking arrhythmogenic right ventricular dysplasia
- Christina Maria Steger1,
- Thomas Hager2,
- Herwig Antretter1,
- Hans Xaver Hoyer3,
- Johann Altenberger3,
- Gerhard Pölzl1,
- Ludwig Müller1,
- Daniel Höfer1
- 1Innsbruck Medical University, Cardiac Surgery, Anichstrasse 35, Innsbruck, 6020, Austria
- 2Innsbruck Medical University, Pathology, Müllerstrasse 44, Innsbruck, 6020, Austria
- 3Landeskrankenhaus Salzburg, Cardiology, Müllner Hauptstrasse 48, Salzburg, 5020, Austria
- Christina Maria Steger, Christina.M.Steger{at}i-med.ac.at
- Published 18 November 2009
Summary
Isolated manifestation of sarcoidosis in the heart is very rare. The present work describes the case of a 41-year-old woman with ventricular tachycardia and severe symptoms of heart failure in June 2006. Clinical, MRI and echocardiographic findings revealed the diagnosis of an arrhythmogenic right ventricular dysplasia. Due to the severe progression of the disease, cardiac transplantation was performed in August 2007. Histopathological examination of the explanted heart, however, revealed numerous non-necrotising granulomas with giant cells, lymphocytic infiltration and interstitial fibrosis, finally confirming the diagnosis of a myocardial sarcoidosis.
Footnotes
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Competing interests: None.
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Patient consent: Patient/guardian consent was obtained for publication
