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BMJ Case Reports 2009; doi:10.1136/bcr.08.2008.0792
  • Rare disease

Non-traumatic splenic rupture in a patient with Kasabach–Merritt syndrome

  1. Jitesh Parmar1,
  2. Behnam Shaygi2,
  3. Mike Nelson1
  1. 1
    St Mary’s Hospital, General Surgery, Parkhurst Road, Newport, Isle of Wight PO30 5TG, UK
  2. 2
    King’s College Hospital, Cardio-Thoracic Surgery, Denmark Hill, London SE5 9RS, UK
  1. bshayegi{at}yahoo.com
  • Published 5 March 2009

Summary

This report presents a case illustrating the complications of Kasabach–Merritt syndrome in a 22-year-old man. The patient presented with acute abdominal pain and profound anaemia; a CT scan revealed intraperitoneal bleeding from spontaneous splenic rupture. The patient underwent initial emergency laparotomy and splenectomy, with a subsequent further laparotomy to control haemorrhage. Blood products requirements were extensive: 28 units red blood cells, 14 units fresh frozen plasma, 10 units platelets, 10 units cryoprecipitate and 2× Novo VII. He was then transferred to a nearby tertiary care unit for further management to control his coagulaopathy and he made a full recovery after 4 weeks.

Footnotes

  • Competing interests: none.

  • Patient consent: Patient/guardian consent was obtained for publication.

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