Congenital laryngomucocoele: a rare cause for CHAOS
- 1Hospital Fernando Fonseca, Pediatrics, IC 19, Amadora, 2720-276, Portugal
- 2Hospital Fernando Fonseca, Anatomia Patológica, IC 19, Amadora, 2720-276, Portugal
- 3University Hospital Lund, OB/GYN - Developmental Pathology, University Hospital Lund, Lund, 221 85, Sweden
- Published 27 February 2009
Congenital high airway obstruction syndrome (CHAOS) is a rare but life-threatening condition that results from the obstruction of the upper airways.
We describe a female newborn, from a Grávida II, Para 0, 36-year-old woman, with a routine ultrasound at 30 weeks’ gestation that showed polyhydramnios. She delivered a live-born female baby at 36 weeks without any dismorphic features but with respiratory distress. Attempts at endotracheal intubation were unsuccessful due to the presence of a mass obstructing the larynx. The reanimation process was stopped after 20 minutes. Post-mortem examination demonstrated the presence of a total occlusion of the larynx by a laryngomucocoele. Laryngocele, a congenital cyst of the larynx, occurs rarely and hardly ever as a cause of CHAOS. What is more, laryngomucocoele has not been previously reported as a cause of CHAOS. These conditions represent a neonatal emergency with reserved prognosis unless diagnosed antenatally allowing for a programmed ex utero intrapartum treatment (EXIT) by performing tracheostomy while maintaining the placental circulation.
Competing interests: none.